Diagnosis Code

E76.219 MORQUIO MUCOPOLYSACCHARIDOSES, UNSPECIFIED


Code Information

Diagnosis Code: E76.219

Short Description: Morquio mucopolysaccharidoses, unspecified

Long Description: Morquio mucopolysaccharidoses, unspecified

The code E76.219 is VALID for claim submission

Code Classification:

  • Endocrine, nutritional and metabolic diseases (E00–E89)
    • Metabolic disorders (E70-E88)
      • Disorders of glycosaminoglycan metabolism (E76)
        • E76.219 Morquio mucopolysaccharidoses, unspecified

Code Version: 2022 ICD-10-CM


Synonyms

  • Congenital osteodystrophy
  • Morquio syndrome

References to Index of Diseases and Injuries

The code E76.219 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Morquio syndrome
    • Mucopolysaccharidosis, type IV

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E76.219 Right Arrow 277.5 Mucopolysaccharidosis

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E76 Disorders of glycosaminoglycan metabolism
E76.0 Mucopolysaccharidosis, type I
E76.01 Hurler's syndrome
E76.02 Hurler-Scheie syndrome
E76.03 Scheie's syndrome
E76.1 Mucopolysaccharidosis, type II
E76.2 Other mucopolysaccharidoses
E76.21 Morquio mucopolysaccharidoses
E76.210 Morquio A mucopolysaccharidoses
E76.211 Morquio B mucopolysaccharidoses
E76.22 Sanfilippo mucopolysaccharidoses
E76.29 Other mucopolysaccharidoses
E76.3 Mucopolysaccharidosis, unspecified
E76.8 Other disorders of glucosaminoglycan metabolism
E76.9 Glucosaminoglycan metabolism disorder, unspecified


This page was last updated on: 10/1/2023