Diagnosis Code

G11.3 CEREBELLAR ATAXIA WITH DEFECTIVE DNA REPAIR


Code Information

Diagnosis Code: G11.3

Short Description: Cerebellar ataxia with defective DNA repair

Long Description: Cerebellar ataxia with defective DNA repair

The code G11.3 is VALID for claim submission

Code Classification:

  • Diseases of the nervous system (G00–G99)
    • Systemic atrophies primarily affecting the central nervous system (G10-G14)
      • Hereditary ataxia (G11)
        • G11.3 Cerebellar ataxia with defective DNA repair

Code Version: 2022 ICD-10-CM


Synonyms

  • Ataxia telangiectasia variant
  • Ataxia-telangiectasia syndrome
  • Chorea due to ataxia telangiectasia syndrome
  • Chorea due to immunological disorder

References to Index of Diseases and Injuries

The code G11.3 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Ataxia telangiectasia [Louis-Bar]
  • Type 2 Excludes Notes:
    • Cockayne's syndrome (@Q87.19*)
    • other disorders of purine and pyrimidine metabolism (@E79*.-)
    • xeroderma pigmentosum (@Q82.1*)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
G11.3 Right Arrow 334.8 Spinocerebellar dis NEC

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
G11 Hereditary ataxia
G11.0 Congenital nonprogressive ataxia
G11.1 Early-onset cerebellar ataxia
G11.10 Early-onset cerebellar ataxia, unspecified
G11.11 Friedreich ataxia
G11.19 Other early-onset cerebellar ataxia
G11.2 Late-onset cerebellar ataxia
G11.4 Hereditary spastic paraplegia
G11.5 Hypomyelination - hypogonadotropic hypogonadism - hypodontia
G11.6 Leukodystrophy with vanishing white matter disease
G11.8 Other hereditary ataxias
G11.9 Hereditary ataxia, unspecified


This page was last updated on: 10/1/2023