Diagnosis Code

G11.9 HEREDITARY ATAXIA, UNSPECIFIED


Code Information

Diagnosis Code: G11.9

Short Description: Hereditary ataxia, unspecified

Long Description: Hereditary ataxia, unspecified

The code G11.9 is VALID for claim submission

Code Classification:

  • Diseases of the nervous system (G00–G99)
    • Systemic atrophies primarily affecting the central nervous system (G10-G14)
      • Hereditary ataxia (G11)
        • G11.9 Hereditary ataxia, unspecified

Code Version: 2022 ICD-10-CM


Synonyms

  • Ataxia due to mitochondrial mutations
  • Ataxia with deafness and intellectual disability syndrome
  • Ataxia with tapetoretinal degeneration syndrome
  • Autosomal dominant cerebellar ataxia, deafness and narcolepsy syndrome
  • Autosomal recessive ataxia due to ubiquinone deficiency
  • Autosomal recessive cerebellar ataxia due to STUB1 deficiency
  • Autosomal recessive cerebellar ataxia with oculomotor apraxia type 1
  • Autosomal recessive cerebellar ataxia with oculomotor apraxia type 2
  • Autosomal recessive cerebellar ataxia, epilepsy, intellectual disability syndrome due to RUBCN deficiency
  • Autosomal recessive cerebellar ataxia, epilepsy, intellectual disability syndrome due to TUD deficiency
  • Boucher Neuhäuser syndrome
  • Cerebellar ataxia
  • Cerebellar ataxia and ectodermal dysplasia
  • Cerebellar ataxia with oculomotor apraxia type 4
  • Cerebellar ataxia, areflexia, pes cavus, optic atrophy, sensorineural hearing loss syndrome
  • Cerebral ataxia
  • Chorea due to hereditary ataxia
  • Choreoathetosis
  • Chronic deafness
  • Congenital cataract with ataxia and deafness syndrome
  • Cutaneous syndrome with ichthyosis
  • Early-onset progressive neurodegeneration, blindness, ataxia, spasticity syndrome
  • Episodic ataxia
  • Episodic ataxia type 7
  • Fragile X associated tremor ataxia syndrome
  • Gemignani syndrome
  • Hereditary ataxia
  • Hereditary cerebellar atrophy
  • Hereditary cerebellar degeneration
  • Ichthyosis, cerebellar degeneration and hepatosplenomegaly
  • Infantile cerebellar and retinal degeneration
  • Myoclonus, cerebellar ataxia, deafness syndrome
  • Narcolepsy
  • Optic atrophy, ataxia, peripheral neuropathy, global developmental delay syndrome
  • Paroxysmal choreoathetosis
  • Paroxysmal dystonia
  • Paroxysmal dystonic choreoathetosis with episodic ataxia and spasticity
  • Posthemiplegic ataxia
  • Primary cerebellar degeneration
  • Primary hypersomnia
  • Primary progressive cerebellar degeneration
  • Progressive cerebellar ataxia
  • PUM1-associated developmental disability, ataxia, seizure syndrome
  • Retinal pigment epithelial dystrophy
  • Retinitis pigmentosa-deafness syndrome
  • Retinitis pigmentosa-deafness-ataxia syndrome
  • Saldino-Mainzer dysplasia
  • Seizure, sensorineural deafness, ataxia, intellectual disability, electrolyte imbalance syndrome
  • Spinocerebellar disease
  • X-linked progressive cerebellar ataxia

References to Index of Diseases and Injuries

The code G11.9 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Hereditary cerebellar ataxia NOS
    • Hereditary cerebellar degeneration
    • Hereditary cerebellar disease
    • Hereditary cerebellar syndrome

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
G11.9 Right Arrow 334.9 Spinocerebellar dis NOS

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
G11 Hereditary ataxia
G11.0 Congenital nonprogressive ataxia
G11.1 Early-onset cerebellar ataxia
G11.10 Early-onset cerebellar ataxia, unspecified
G11.11 Friedreich ataxia
G11.19 Other early-onset cerebellar ataxia
G11.2 Late-onset cerebellar ataxia
G11.3 Cerebellar ataxia with defective DNA repair
G11.4 Hereditary spastic paraplegia
G11.5 Hypomyelination - hypogonadotropic hypogonadism - hypodontia
G11.6 Leukodystrophy with vanishing white matter disease
G11.8 Other hereditary ataxias


This page was last updated on: 10/1/2023