Diagnosis Code

G11.4 HEREDITARY SPASTIC PARAPLEGIA


Code Information

Diagnosis Code: G11.4

Short Description: Hereditary spastic paraplegia

Long Description: Hereditary spastic paraplegia

The code G11.4 is VALID for claim submission

Code Classification:

  • Diseases of the nervous system (G00–G99)
    • Systemic atrophies primarily affecting the central nervous system (G10-G14)
      • Hereditary ataxia (G11)
        • G11.4 Hereditary spastic paraplegia

Code Version: 2022 ICD-10-CM


Synonyms

  • Autosomal dominant complex hereditary spastic paraplegia
  • Autosomal dominant complex hereditary spastic paraplegia
  • Autosomal dominant complex hereditary spastic paraplegia
  • Autosomal dominant complex hereditary spastic paraplegia
  • Autosomal dominant complex hereditary spastic paraplegia
  • Autosomal dominant distal hereditary motor neuropathy
  • Autosomal dominant hereditary spastic paraplegia
  • Autosomal dominant spastic ataxia type 1
  • Autosomal dominant spastic paraplegia type 10
  • Autosomal dominant spastic paraplegia type 12
  • Autosomal dominant spastic paraplegia type 13
  • Autosomal dominant spastic paraplegia type 17
  • Autosomal dominant spastic paraplegia type 19
  • Autosomal dominant spastic paraplegia type 29
  • Autosomal dominant spastic paraplegia type 3
  • Autosomal dominant spastic paraplegia type 31
  • Autosomal dominant spastic paraplegia type 36
  • Autosomal dominant spastic paraplegia type 37
  • Autosomal dominant spastic paraplegia type 38
  • Autosomal dominant spastic paraplegia type 4
  • Autosomal dominant spastic paraplegia type 41
  • Autosomal dominant spastic paraplegia type 42
  • Autosomal dominant spastic paraplegia type 6
  • Autosomal dominant spastic paraplegia type 73
  • Autosomal dominant spastic paraplegia type 8
  • Autosomal dominant spastic paraplegia type 9A
  • Autosomal dominant spastic paraplegia type 9B
  • Autosomal recessive cerebellar ataxia with late-onset spasticity
  • Autosomal recessive complex spastic paraplegia due to Kennedy pathway dysfunction
  • Autosomal recessive hereditary spastic paraplegia
  • Autosomal recessive spastic ataxia of Charlevoix-Saguenay
  • Autosomal recessive spastic ataxia with leukoencephalopathy
  • Autosomal recessive spastic ataxia, optic atrophy, dysarthria syndrome
  • Autosomal recessive spastic paraplegia type 11
  • Autosomal recessive spastic paraplegia type 14
  • Autosomal recessive spastic paraplegia type 15
  • Autosomal recessive spastic paraplegia type 18
  • Autosomal recessive spastic paraplegia type 21
  • Autosomal recessive spastic paraplegia type 23
  • Autosomal recessive spastic paraplegia type 24
  • Autosomal recessive spastic paraplegia type 25
  • Autosomal recessive spastic paraplegia type 26
  • Autosomal recessive spastic paraplegia type 27
  • Autosomal recessive spastic paraplegia type 28
  • Autosomal recessive spastic paraplegia type 32
  • Autosomal recessive spastic paraplegia type 35
  • Autosomal recessive spastic paraplegia type 39
  • Autosomal recessive spastic paraplegia type 43
  • Autosomal recessive spastic paraplegia type 44
  • Autosomal recessive spastic paraplegia type 45
  • Autosomal recessive spastic paraplegia type 46
  • Autosomal recessive spastic paraplegia type 48
  • Autosomal recessive spastic paraplegia type 53
  • Autosomal recessive spastic paraplegia type 54
  • Autosomal recessive spastic paraplegia type 55
  • Autosomal recessive spastic paraplegia type 56
  • Autosomal recessive spastic paraplegia type 57
  • Autosomal recessive spastic paraplegia type 58
  • Autosomal recessive spastic paraplegia type 59
  • Autosomal recessive spastic paraplegia type 5A
  • Autosomal recessive spastic paraplegia type 60
  • Autosomal recessive spastic paraplegia type 61
  • Autosomal recessive spastic paraplegia type 62
  • Autosomal recessive spastic paraplegia type 63
  • Autosomal recessive spastic paraplegia type 64
  • Autosomal recessive spastic paraplegia type 66
  • Autosomal recessive spastic paraplegia type 67
  • Autosomal recessive spastic paraplegia type 69
  • Autosomal recessive spastic paraplegia type 70
  • Autosomal recessive spastic paraplegia type 71
  • Autosomal recessive spastic paraplegia type 74
  • Autosomal recessive spastic paraplegia type 75
  • Autosomal recessive spastic paraplegia type 76
  • Autosomal recessive spastic paraplegia type 77
  • Autosomal recessive spastic paraplegia type 78
  • Autosomal recessive spastic paraplegia type 9B
  • Autosomal spastic paraplegia type 30
  • Autosomal spastic paraplegia type 72
  • Bedouin spastic ataxia syndrome
  • Bilateral lower limb ataxia
  • Choreoathetosis
  • Chronic deafness
  • Complicated hereditary spastic paraplegia
  • Congenital miosis
  • Constricted pupil
  • Disorder of glutamine metabolism
  • Distal spinal muscular atrophy
  • Early-onset progressive encephalopathy, spastic ataxia, distal spinal muscular atrophy syndrome
  • Early-onset spastic ataxia, myoclonic epilepsy, neuropathy syndrome
  • Fryns macrocephaly
  • Hereditary sensory and autonomic neuropathy with spastic paraplegia
  • Hereditary spastic paraplegia
  • Infantile ascending hereditary spastic paralysis
  • Kyphoscoliosis, lateral tongue atrophy, hereditary spastic paraplegia syndrome
  • Macular corneal dystrophy
  • Maternally inherited mitochondrial deoxyribonucleic acid disease
  • Motor neuron disease due to hereditary spastic paraplegia
  • MT-ATP6-related mitochondrial spastic paraplegia
  • Palmoplantar keratoderma, spastic paralysis syndrome
  • Parkinsonism due to hereditary spastic paraplegia
  • Parkinsonism due to heredodegenerative disorder
  • Paroxysmal choreoathetosis
  • Paroxysmal dystonia
  • Paroxysmal dystonic choreoathetosis with episodic ataxia and spasticity
  • Progressive muscular atrophy
  • Punctate palmoplantar keratoderma
  • Pure hereditary spastic paraplegia
  • Second cranial nerve finding
  • Second cranial nerve finding
  • Second cranial nerve finding
  • Second cranial nerve finding
  • Second cranial nerve finding
  • Second cranial nerve finding
  • Second cranial nerve finding
  • Severe intellectual disability and progressive spastic paraplegia
  • Spastic ataxia with congenital miosis
  • Spastic ataxia, dysarthria due to glutaminase deficiency
  • Spastic paraparesis
  • Spastic paraparesis and deafness
  • Spastic paraplegia type 7
  • Spastic paraplegia with Paget disease of bone syndrome
  • Spastic paraplegia with precocious puberty syndrome
  • Spastic paraplegia, facial cutaneous lesion syndrome
  • Spastic paraplegia, glaucoma, intellectual disability syndrome
  • Spastic paraplegia, nephritis, deafness syndrome
  • Spastic paraplegia, neuropathy, poikiloderma syndrome
  • Spastic paraplegia, optic atrophy, neuropathy syndrome
  • Spastic paraplegia, severe developmental delay, epilepsy syndrome
  • SPOAN and SPOAN-related disorder
  • SPOAN and SPOAN-related disorder
  • SPOAN and SPOAN-related disorder
  • SPOAN and SPOAN-related disorder
  • SPOAN and SPOAN-related disorder
  • X-linked complex hereditary spastic paraplegia
  • X-linked hereditary spastic paraplegia
  • X-linked pure hereditary spastic paraplegia
  • X-linked spastic paraplegia type 16
  • X-linked spastic paraplegia type 2
  • X-linked spastic paraplegia type 34

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
G11.4 Right Arrow 334.1 Hered spastic paraplegia

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
G11 Hereditary ataxia
G11.0 Congenital nonprogressive ataxia
G11.1 Early-onset cerebellar ataxia
G11.10 Early-onset cerebellar ataxia, unspecified
G11.11 Friedreich ataxia
G11.19 Other early-onset cerebellar ataxia
G11.2 Late-onset cerebellar ataxia
G11.3 Cerebellar ataxia with defective DNA repair
G11.5 Hypomyelination - hypogonadotropic hypogonadism - hypodontia
G11.6 Leukodystrophy with vanishing white matter disease
G11.8 Other hereditary ataxias
G11.9 Hereditary ataxia, unspecified


This page was last updated on: 10/1/2023