E75.240 NIEMANN-PICK DISEASE TYPE A

Code Information

  • Diagnosis Code: E75.240
  • Short Description: Niemann-Pick disease type A
  • Long Description: Niemann-Pick disease type A
  • Code Version: 2025 ICD-10-CM

The code E75.240 is VALID for claim submission

Code Classification

Synonyms

  • Lipoidosis
  • Niemann-Pick disease, type A
  • Sphingomyelin/cholesterol lipidosis

References to Index of Diseases and Injuries

The code E75.240 has the following ICD-10-CM references to the Index of Diseases and Injuries

  • Inclusion Terms:
    • Acid sphingomyelinase deficiency type A (ASMD type A)
    • Infantile neurovisceral acid sphingomyelinase deficiency

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E75.240 Right Arrow 272.7 Lipidoses
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E75 Disorders of sphingolipid metabolism and other lipid storage disorders
E75.0 GM2 gangliosidosis
E75.00 GM2 gangliosidosis, unspecified
E75.01 Sandhoff disease
E75.02 Tay-Sachs disease
E75.09 Other GM2 gangliosidosis
E75.1 Other and unspecified gangliosidosis
E75.10 Unspecified gangliosidosis
E75.11 Mucolipidosis IV
E75.19 Other gangliosidosis
E75.2 Other sphingolipidosis
E75.21 Fabry (-Anderson) disease
E75.22 Gaucher disease
E75.23 Krabbe disease
E75.24 Niemann-Pick disease
E75.241 Niemann-Pick disease type B
E75.242 Niemann-Pick disease type C
E75.243 Niemann-Pick disease type D
E75.244 Niemann-Pick disease type A/B
E75.248 Other Niemann-Pick disease
E75.249 Niemann-Pick disease, unspecified
E75.25 Metachromatic leukodystrophy
E75.26 Sulfatase deficiency
E75.27 Pelizaeus-Merzbacher disease
E75.28 Canavan disease
E75.29 Other sphingolipidosis
E75.3 Sphingolipidosis, unspecified
E75.4 Neuronal ceroid lipofuscinosis
E75.5 Other lipid storage disorders
E75.6 Lipid storage disorder, unspecified
This page was last updated on: 10/1/2025
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