E75.6 LIPID STORAGE DISORDER, UNSPECIFIED

Code Information

  • Diagnosis Code: E75.6
  • Short Description: Lipid storage disorder, unspecified
  • Long Description: Lipid storage disorder, unspecified
  • Code Version: 2025 ICD-10-CM

The code E75.6 is VALID for claim submission

Code Classification

Synonyms

  • Abnormal lipid deposits
  • Cerebral degeneration associated with generalized lipidosis
  • Hereditary retinal dystrophies in lipidoses
  • Hereditary retinal dystrophies in lipidoses
  • Lipid storage disease
  • Lipid storage myopathy
  • Lipoidosis
  • Mitochondrial-lipid-glycogen storage myopathy
  • Retinal dystrophy in cerebroretinal lipidosis
  • Retinal dystrophy in systemic lipidosis

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E75.6 Right Arrow 272.9 Lipoid metabol dis NOS
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E75 Disorders of sphingolipid metabolism and other lipid storage disorders
E75.0 GM2 gangliosidosis
E75.00 GM2 gangliosidosis, unspecified
E75.01 Sandhoff disease
E75.02 Tay-Sachs disease
E75.09 Other GM2 gangliosidosis
E75.1 Other and unspecified gangliosidosis
E75.10 Unspecified gangliosidosis
E75.11 Mucolipidosis IV
E75.19 Other gangliosidosis
E75.2 Other sphingolipidosis
E75.21 Fabry (-Anderson) disease
E75.22 Gaucher disease
E75.23 Krabbe disease
E75.24 Niemann-Pick disease
E75.240 Niemann-Pick disease type A
E75.241 Niemann-Pick disease type B
E75.242 Niemann-Pick disease type C
E75.243 Niemann-Pick disease type D
E75.244 Niemann-Pick disease type A/B
E75.248 Other Niemann-Pick disease
E75.249 Niemann-Pick disease, unspecified
E75.25 Metachromatic leukodystrophy
E75.26 Sulfatase deficiency
E75.27 Pelizaeus-Merzbacher disease
E75.28 Canavan disease
E75.29 Other sphingolipidosis
E75.3 Sphingolipidosis, unspecified
E75.4 Neuronal ceroid lipofuscinosis
E75.5 Other lipid storage disorders
This page was last updated on: 10/1/2025