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Taxonomy Codes
E75.25 METACHROMATIC LEUKODYSTROPHY
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ICD-10 List
E00–E89
E70-E88
E75
E75.25
Code Information
Diagnosis Code:
E75.25
Short Description:
Metachromatic leukodystrophy
Long Description:
Metachromatic leukodystrophy
Code Version:
2025 ICD-10-CM
The code E75.25 is VALID for claim submission
Code Classification
Endocrine, nutritional and metabolic diseases (E00–E89)
Metabolic disorders (E70-E88)
Disorders of sphingolipid metabolism and other lipid storage disorders (E75)
Synonyms
Arylsulfatase A deficiency
Dystonia due to metachromatic leucodystrophy
Metachromatic leukodystrophy
Metachromatic leukodystrophy
Metachromatic leukodystrophy due to deficiency of cerebroside sulfatase activator
Metachromatic leukodystrophy without arylsulfatase deficiency
Metachromatic leukodystrophy, adult type
Metachromatic leukodystrophy, congenital type
Metachromatic leukodystrophy, juvenile type
Metachromatic leukodystrophy, late infantile type
Pelizaeus Merzbacher like disease
Sphingolipid activator protein 1 deficiency
Crosswalk Information
ICD-10 Code
ICD-9 Code
ICD-9 Description
E75.25
330.0
Leukodystrophy
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.
Similar Codes
ICD-10 Code
ICD-10 Description
E75
Disorders of sphingolipid metabolism and other lipid storage disorders
E75.0
GM2 gangliosidosis
E75.00
GM2 gangliosidosis, unspecified
E75.01
Sandhoff disease
E75.02
Tay-Sachs disease
E75.09
Other GM2 gangliosidosis
E75.1
Other and unspecified gangliosidosis
E75.10
Unspecified gangliosidosis
E75.11
Mucolipidosis IV
E75.19
Other gangliosidosis
E75.2
Other sphingolipidosis
E75.21
Fabry (-Anderson) disease
E75.22
Gaucher disease
E75.23
Krabbe disease
E75.24
Niemann-Pick disease
E75.240
Niemann-Pick disease type A
E75.241
Niemann-Pick disease type B
E75.242
Niemann-Pick disease type C
E75.243
Niemann-Pick disease type D
E75.244
Niemann-Pick disease type A/B
E75.248
Other Niemann-Pick disease
E75.249
Niemann-Pick disease, unspecified
E75.26
Sulfatase deficiency
E75.27
Pelizaeus-Merzbacher disease
E75.28
Canavan disease
E75.29
Other sphingolipidosis
E75.3
Sphingolipidosis, unspecified
E75.4
Neuronal ceroid lipofuscinosis
E75.5
Other lipid storage disorders
E75.6
Lipid storage disorder, unspecified
This page was last updated on: 10/1/2025
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