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Diagnosis Code

D80.0 HEREDITARY HYPOGAMMAGLOBULINEMIA


Code Information

Diagnosis Code: D80.0

Short Description: Hereditary hypogammaglobulinemia

Long Description: Hereditary hypogammaglobulinemia

The code D80.0 is VALID for claim submission

Code Classification:

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
    • Certain disorders involving the immune mechanism (D80-D89)
      • Immunodeficiency with predominantly antibody defects (D80)
        • D80.0 Hereditary hypogammaglobulinemia

Code Version: 2022 ICD-10-CM


Synonyms

  • Agammaglobulinemia, microcephaly, craniosynostosis, severe dermatitis syndrome
  • Autosomal agammaglobulinemia with absent B-cells
  • B-cell immunodeficiency, limb anomaly, urogenital malformation syndrome
  • Congenital agammaglobulinemia
  • Congenital agammaglobulinemia
  • Congenital agammaglobulinemia
  • Congenital hypogammaglobulinemia
  • Congenital hypogammaglobulinemia
  • Hypogammaglobulinemia
  • Hypogammaglobulinemia
  • Hypogammaglobulinemia
  • Infantile-onset pulmonary alveolar proteinosis, hypogammaglobulinemia
  • Isolated agammaglobulinemia
  • Microcephaly, hypogammaglobulinemia, abnormal immunity syndrome
  • Osteopetrosis hypogammaglobulinemia syndrome
  • Proteinosis
  • Pulmonary alveolar proteinosis
  • Specific antibody deficiency
  • X-linked agammaglobulinemia
  • X-linked agammaglobulinemia with growth hormone deficiency
  • X-linked intellectual disability with hypogammaglobulinemia and progressive neurological deterioration syndrome

Diagnostic Related Group(s)

The code D80.0 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Reticuloendothelial And Immunity Disorders With Mcc (814)
  • Reticuloendothelial And Immunity Disorders With Cc (815)
  • Reticuloendothelial And Immunity Disorders Without Cc/mcc (816)

References to Index of Diseases and Injuries

The code D80.0 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Autosomal recessive agammaglobulinemia (Swiss type)
    • X-linked agammaglobulinemia [Bruton] (with growth hormone deficiency)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
D80.0 Right Arrow 279.04 Cong hypogammaglobulinem

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
D80 Immunodeficiency with predominantly antibody defects
D80.1 Nonfamilial hypogammaglobulinemia
D80.2 Selective deficiency of immunoglobulin A [IgA]
D80.3 Selective deficiency of immunoglobulin G [IgG] subclasses
D80.4 Selective deficiency of immunoglobulin M [IgM]
D80.5 Immunodeficiency with increased immunoglobulin M [IgM]
D80.6 Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia
D80.7 Transient hypogammaglobulinemia of infancy
D80.8 Other immunodeficiencies with predominantly antibody defects
D80.9 Immunodeficiency with predominantly antibody defects, unspecified

This page was last updated on: 10/1/2023

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