Diagnosis Code

E75.249 NIEMANN-PICK DISEASE, UNSPECIFIED


Code Information

Diagnosis Code: E75.249

Short Description: Niemann-Pick disease, unspecified

Long Description: Niemann-Pick disease, unspecified

The code E75.249 is VALID for claim submission

Code Classification:

  • Endocrine, nutritional and metabolic diseases (E00–E89)
    • Metabolic disorders (E70-E88)
      • Disord of sphingolipid metab and oth lipid storage disorders (E75)
        • E75.249 Niemann-Pick disease, unspecified

Code Version: 2022 ICD-10-CM


Synonyms

  • Cerebral degeneration associated with generalized lipidosis
  • Cerebral degeneration in Niemann-Pick disease
  • Lipoidosis
  • Sphingomyelin/cholesterol lipidosis

References to Index of Diseases and Injuries

The code E75.249 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Acid sphingomyelinase deficiency (ASMD) NOS

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E75.249 Right Arrow 272.7 Lipidoses

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E75 Disorders of sphingolipid metabolism and other lipid storage disorders
E75.0 GM2 gangliosidosis
E75.00 GM2 gangliosidosis, unspecified
E75.01 Sandhoff disease
E75.02 Tay-Sachs disease
E75.09 Other GM2 gangliosidosis
E75.1 Other and unspecified gangliosidosis
E75.10 Unspecified gangliosidosis
E75.11 Mucolipidosis IV
E75.19 Other gangliosidosis
E75.2 Other sphingolipidosis
E75.21 Fabry (-Anderson) disease
E75.22 Gaucher disease
E75.23 Krabbe disease
E75.24 Niemann-Pick disease
E75.240 Niemann-Pick disease type A
E75.241 Niemann-Pick disease type B
E75.242 Niemann-Pick disease type C
E75.243 Niemann-Pick disease type D
E75.244 Niemann-Pick disease type A/B
E75.248 Other Niemann-Pick disease
E75.25 Metachromatic leukodystrophy
E75.26 Sulfatase deficiency
E75.27 Pelizaeus-Merzbacher disease
E75.28 Canavan disease
E75.29 Other sphingolipidosis
E75.3 Sphingolipidosis, unspecified
E75.4 Neuronal ceroid lipofuscinosis
E75.5 Other lipid storage disorders
E75.6 Lipid storage disorder, unspecified


This page was last updated on: 10/1/2023