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Taxonomy Codes
E75.3 SPHINGOLIPIDOSIS, UNSPECIFIED
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ICD-10 List
E00–E89
E70-E88
E75
E75.3
Code Information
Diagnosis Code:
E75.3
Short Description:
Sphingolipidosis, unspecified
Long Description:
Sphingolipidosis, unspecified
Code Version:
2025 ICD-10-CM
The code E75.3 is VALID for claim submission
Code Classification
Endocrine, nutritional and metabolic diseases (E00–E89)
Metabolic disorders (E70-E88)
Disorders of sphingolipid metabolism and other lipid storage disorders (E75)
Synonyms
Sphingolipidosis
Crosswalk Information
ICD-10 Code
ICD-9 Code
ICD-9 Description
E75.3
272.7
Lipidoses
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.
Similar Codes
ICD-10 Code
ICD-10 Description
E75
Disorders of sphingolipid metabolism and other lipid storage disorders
E75.0
GM2 gangliosidosis
E75.00
GM2 gangliosidosis, unspecified
E75.01
Sandhoff disease
E75.02
Tay-Sachs disease
E75.09
Other GM2 gangliosidosis
E75.1
Other and unspecified gangliosidosis
E75.10
Unspecified gangliosidosis
E75.11
Mucolipidosis IV
E75.19
Other gangliosidosis
E75.2
Other sphingolipidosis
E75.21
Fabry (-Anderson) disease
E75.22
Gaucher disease
E75.23
Krabbe disease
E75.24
Niemann-Pick disease
E75.240
Niemann-Pick disease type A
E75.241
Niemann-Pick disease type B
E75.242
Niemann-Pick disease type C
E75.243
Niemann-Pick disease type D
E75.244
Niemann-Pick disease type A/B
E75.248
Other Niemann-Pick disease
E75.249
Niemann-Pick disease, unspecified
E75.25
Metachromatic leukodystrophy
E75.26
Sulfatase deficiency
E75.27
Pelizaeus-Merzbacher disease
E75.28
Canavan disease
E75.29
Other sphingolipidosis
E75.4
Neuronal ceroid lipofuscinosis
E75.5
Other lipid storage disorders
E75.6
Lipid storage disorder, unspecified
This page was last updated on: 10/1/2024
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