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Taxonomy Codes
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Certain disorders involving the immune mechanism (D80-D89)
Combined immunodeficiencies (D81)
D81
- Combined immunodeficiencies
D81.0
- Severe combined immunodeficiency with reticular dysgenesis
D81.1
- Severe combined immunodeficiency w low T- and B-cell numbers
D81.2
- Severe combined immunodef w low or normal B-cell numbers
D81.3
- Adenosine deaminase [ADA] deficiency
D81.30
- Adenosine deaminase deficiency, unspecified
D81.31
- Severe combined immunodef due to adenosine deaminase defic
D81.32
- Adenosine deaminase 2 deficiency
D81.39
- Other adenosine deaminase deficiency
D81.4
- Nezelof's syndrome
D81.5
- Purine nucleoside phosphorylase [PNP] deficiency
D81.6
- Major histocompatibility complex class I deficiency
D81.7
- Major histocompatibility complex class II deficiency
D81.8
- Other combined immunodeficiencies
D81.81
- Biotin-dependent carboxylase deficiency
D81.810
- Biotinidase deficiency
D81.818
- Other biotin-dependent carboxylase deficiency
D81.819
- Biotin-dependent carboxylase deficiency, unspecified
D81.82
- Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]
D81.89
- Other combined immunodeficiencies
D81.9
- Combined immunodeficiency, unspecified