Diagnosis Code

D81.39 OTHER ADENOSINE DEAMINASE DEFICIENCY


Code Information

Diagnosis Code: D81.39

Short Description: Other adenosine deaminase deficiency

Long Description: Other adenosine deaminase deficiency

The code D81.39 is VALID for claim submission

Code Classification:

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
    • Certain disorders involving the immune mechanism (D80-D89)
      • Combined immunodeficiencies (D81)
        • D81.39 Other adenosine deaminase deficiency

Code Version: 2022 ICD-10-CM


References to Index of Diseases and Injuries

The code D81.39 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Adenosine deaminase [ADA] deficiency type 1, NOS
    • Adenosine deaminase [ADA] deficiency type 1, without SCID
    • Adenosine deaminase [ADA] deficiency type 1, without severe combined immunodeficiency
    • Partial ADA deficiency (type 1)
    • Partial adenosine deaminase deficiency (type 1)

Similar Codes

ICD-10 Code ICD-10 Description
D81 Combined immunodeficiencies
D81.0 Severe combined immunodeficiency [SCID] with reticular dysgenesis
D81.1 Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
D81.2 Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
D81.3 Adenosine deaminase [ADA] deficiency
D81.30 Adenosine deaminase deficiency, unspecified
D81.31 Severe combined immunodeficiency due to adenosine deaminase deficiency
D81.32 Adenosine deaminase 2 deficiency
D81.4 Nezelof's syndrome
D81.5 Purine nucleoside phosphorylase [PNP] deficiency
D81.6 Major histocompatibility complex class I deficiency
D81.7 Major histocompatibility complex class II deficiency
D81.8 Other combined immunodeficiencies
D81.81 Biotin-dependent carboxylase deficiency
D81.810 Biotinidase deficiency
D81.818 Other biotin-dependent carboxylase deficiency
D81.819 Biotin-dependent carboxylase deficiency, unspecified
D81.82 Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]
D81.89 Other combined immunodeficiencies
D81.9 Combined immunodeficiency, unspecified


This page was last updated on: 10/1/2023