D81.81 BIOTIN-DEPENDENT CARBOXYLASE DEFICIENCY

Code Information

Diagnosis Code: D81.81

Short Description: Biotin-dependent carboxylase deficiency

Long Description: Biotin-dependent carboxylase deficiency

The code D81.81 is NOT VALID for claim submission

Code Classification:

Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
- Certain disorders involving the immune mechanism (D80-D89)
  - Combined immunodeficiencies (D81)
    - D81.81 Biotin-dependent carboxylase deficiency

Code Version: 2022 ICD-10-CM

The code D81.81 has the following ICD-10-CM references to the Index of Diseases and Injuries

Inclusion Terms:
- Multiple carboxylase deficiency
Type 1 Excludes Notes:
- biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (@E53.8*)

ICD-10 Code	ICD-10 Description
D81	Combined immunodeficiencies
D81.0	Severe combined immunodeficiency [SCID] with reticular dysgenesis
D81.1	Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
D81.2	Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
D81.3	Adenosine deaminase [ADA] deficiency
D81.30	Adenosine deaminase deficiency, unspecified
D81.31	Severe combined immunodeficiency due to adenosine deaminase deficiency
D81.32	Adenosine deaminase 2 deficiency
D81.39	Other adenosine deaminase deficiency
D81.4	Nezelof's syndrome
D81.5	Purine nucleoside phosphorylase [PNP] deficiency
D81.6	Major histocompatibility complex class I deficiency
D81.7	Major histocompatibility complex class II deficiency
D81.8	Other combined immunodeficiencies
D81.810	Biotinidase deficiency
D81.818	Other biotin-dependent carboxylase deficiency
D81.819	Biotin-dependent carboxylase deficiency, unspecified
D81.82	Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]
D81.89	Other combined immunodeficiencies
D81.9	Combined immunodeficiency, unspecified

This page was last updated on: 10/1/2023