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Diagnosis Code

D81.89 OTHER COMBINED IMMUNODEFICIENCIES


Code Information

Diagnosis Code: D81.89

Short Description: Other combined immunodeficiencies

Long Description: Other combined immunodeficiencies

The code D81.89 is VALID for claim submission

Code Classification:

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
    • Certain disorders involving the immune mechanism (D80-D89)
      • Combined immunodeficiencies (D81)
        • D81.89 Other combined immunodeficiencies

Code Version: 2022 ICD-10-CM


Synonyms

  • Anhidrotic ectodermal dysplasia, immunodeficiency, osteopetrosis, lymphedema syndrome
  • BENTA disease
  • Combined immunodeficiency due to CARMIL2 deficiency
  • Combined immunodeficiency due to CD3gamma deficiency
  • Combined immunodeficiency due to CD70 deficiency
  • Combined immunodeficiency due to CRAC channel dysfunction
  • Combined immunodeficiency due to DOCK8 deficiency
  • Combined immunodeficiency due to GINS1 deficiency
  • Combined immunodeficiency due to interleukin 21 receptor deficiency
  • Combined immunodeficiency due to ITK deficiency
  • Combined immunodeficiency due to LRBA deficiency
  • Combined immunodeficiency due to MALT1 deficiency
  • Combined immunodeficiency due to moesin deficiency
  • Combined immunodeficiency due to OX40 deficiency
  • Combined immunodeficiency due to STK4 deficiency
  • Combined immunodeficiency due to TFRC deficiency
  • Combined immunodeficiency due to ZAP70 deficiency
  • Combined immunodeficiency, enteropathy spectrum
  • DOCK2 deficiency
  • Immunodeficiency by defective expression of human leukocyte antigen class 1
  • Lymphocyte count below reference range
  • Lymphocytopenia
  • Myelokathexis
  • Primary immunodeficiency with multifaceted aberrant lymphoid immunity
  • Primary immunodeficiency with natural killer cell deficiency and adrenal insufficiency
  • RIDDLE syndrome
  • Severe combined immunodeficiency due to CARD11 deficiency
  • Severe combined immunodeficiency due to CORO1A deficiency
  • Severe combined immunodeficiency due to DCLRE1C deficiency
  • Severe combined immunodeficiency due to deoxyribonucleic acid dependent protein kinase catalytic subunit deficiency
  • Severe combined immunodeficiency due to IKK2 deficiency
  • Severe combined immunodeficiency due to LAT deficiency
  • Severe T-cell immunodeficiency, congenital alopecia, nail dystrophy syndrome
  • Susceptibility to respiratory infection associated with CD8alpha chain mutation
  • T-cell negative B-cell positive severe combined immunodeficiency due to JAK3 deficiency
  • T-cell receptor alpha-beta-positive T-cell deficiency
  • Warts, hypogammaglobulinemia, infections, and myelokathexis

Diagnostic Related Group(s)

The code D81.89 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Major Hematological And Immunological Diagnoses Except Sickle Cell Crisis And Coagulation Disorders With Mcc (808)
  • Major Hematological And Immunological Diagnoses Except Sickle Cell Crisis And Coagulation Disorders With Cc (809)
  • Major Hematological And Immunological Diagnoses Except Sickle Cell Crisis And Coagulation Disorders Without Cc/mcc (810)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
D81.89 Right Arrow 279.2 Combined immunity defic

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
D81 Combined immunodeficiencies
D81.0 Severe combined immunodeficiency [SCID] with reticular dysgenesis
D81.1 Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
D81.2 Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
D81.3 Adenosine deaminase [ADA] deficiency
D81.30 Adenosine deaminase deficiency, unspecified
D81.31 Severe combined immunodeficiency due to adenosine deaminase deficiency
D81.32 Adenosine deaminase 2 deficiency
D81.39 Other adenosine deaminase deficiency
D81.4 Nezelof's syndrome
D81.5 Purine nucleoside phosphorylase [PNP] deficiency
D81.6 Major histocompatibility complex class I deficiency
D81.7 Major histocompatibility complex class II deficiency
D81.8 Other combined immunodeficiencies
D81.81 Biotin-dependent carboxylase deficiency
D81.810 Biotinidase deficiency
D81.818 Other biotin-dependent carboxylase deficiency
D81.819 Biotin-dependent carboxylase deficiency, unspecified
D81.82 Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]
D81.9 Combined immunodeficiency, unspecified

This page was last updated on: 10/1/2023

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