| D81 |
Combined immunodeficiencies |
| D81.0 |
Severe combined immunodeficiency [SCID] with reticular dysgenesis |
| D81.1 |
Severe combined immunodeficiency [SCID] with low T- and B-cell numbers |
| D81.2 |
Severe combined immunodeficiency [SCID] with low or normal B-cell numbers |
| D81.3 |
Adenosine deaminase [ADA] deficiency |
| D81.30 |
Adenosine deaminase deficiency, unspecified |
| D81.31 |
Severe combined immunodeficiency due to adenosine deaminase deficiency |
| D81.32 |
Adenosine deaminase 2 deficiency |
| D81.39 |
Other adenosine deaminase deficiency |
| D81.4 |
Nezelof's syndrome |
| D81.5 |
Purine nucleoside phosphorylase [PNP] deficiency |
| D81.6 |
Major histocompatibility complex class I deficiency |
| D81.7 |
Major histocompatibility complex class II deficiency |
| D81.81 |
Biotin-dependent carboxylase deficiency |
| D81.810 |
Biotinidase deficiency |
| D81.818 |
Other biotin-dependent carboxylase deficiency |
| D81.819 |
Biotin-dependent carboxylase deficiency, unspecified |
| D81.82 |
Activated Phosphoinositide 3-kinase Delta Syndrome [APDS] |
| D81.89 |
Other combined immunodeficiencies |
| D81.9 |
Combined immunodeficiency, unspecified |
