D81.818 OTHER BIOTIN-DEPENDENT CARBOXYLASE DEFICIENCY

Code Information

  • Diagnosis Code: D81.818
  • Short Description: Other biotin-dependent carboxylase deficiency
  • Long Description: Other biotin-dependent carboxylase deficiency
  • Code Version: 2025 ICD-10-CM

The code D81.818 is VALID for claim submission

Code Classification

Synonyms

  • Holocarboxylase synthase deficiency
  • Multiple carboxylase deficiency

Diagnostic Related Group(s)

The code D81.818 is grouped in the following Diagnostic Related Group(s) MS-DRG V42.0

  1. Miscellaneous Disorders Of Nutrition, Metabolism, Fluids And Electrolytes With Mcc (640)
  2. Miscellaneous Disorders Of Nutrition, Metabolism, Fluids And Electrolytes Without Mcc (641)

References to Index of Diseases and Injuries

The code D81.818 has the following ICD-10-CM references to the Index of Diseases and Injuries

  • Inclusion Terms:
    • Holocarboxylase synthetase deficiency
    • Other multiple carboxylase deficiency

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
D81.818 Right Arrow 266.2 B-complex defic NEC
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
D81 Combined immunodeficiencies
D81.0 Severe combined immunodeficiency [SCID] with reticular dysgenesis
D81.1 Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
D81.2 Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
D81.3 Adenosine deaminase [ADA] deficiency
D81.30 Adenosine deaminase deficiency, unspecified
D81.31 Severe combined immunodeficiency due to adenosine deaminase deficiency
D81.32 Adenosine deaminase 2 deficiency
D81.39 Other adenosine deaminase deficiency
D81.4 Nezelof's syndrome
D81.5 Purine nucleoside phosphorylase [PNP] deficiency
D81.6 Major histocompatibility complex class I deficiency
D81.7 Major histocompatibility complex class II deficiency
D81.8 Other combined immunodeficiencies
D81.81 Biotin-dependent carboxylase deficiency
D81.810 Biotinidase deficiency
D81.819 Biotin-dependent carboxylase deficiency, unspecified
D81.82 Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]
D81.89 Other combined immunodeficiencies
D81.9 Combined immunodeficiency, unspecified
This page was last updated on: 10/1/2024