D81.89 OTHER COMBINED IMMUNODEFICIENCIES

Code Information

  • Diagnosis Code: D81.89
  • Short Description: Other combined immunodeficiencies
  • Long Description: Other combined immunodeficiencies
  • Code Version: 2025 ICD-10-CM

The code D81.89 is VALID for claim submission

Code Classification

Synonyms

  • Anhidrotic ectodermal dysplasia, immunodeficiency, osteopetrosis, lymphedema syndrome
  • BENTA disease
  • Combined immunodeficiency due to CARMIL2 deficiency
  • Combined immunodeficiency due to CD3gamma deficiency
  • Combined immunodeficiency due to CD70 deficiency
  • Combined immunodeficiency due to CRAC channel dysfunction
  • Combined immunodeficiency due to DOCK8 deficiency
  • Combined immunodeficiency due to GINS1 deficiency
  • Combined immunodeficiency due to interleukin 21 receptor deficiency
  • Combined immunodeficiency due to ITK deficiency
  • Combined immunodeficiency due to LRBA deficiency
  • Combined immunodeficiency due to MALT1 deficiency
  • Combined immunodeficiency due to moesin deficiency
  • Combined immunodeficiency due to OX40 deficiency
  • Combined immunodeficiency due to STK4 deficiency
  • Combined immunodeficiency due to TFRC deficiency
  • Combined immunodeficiency due to ZAP70 deficiency
  • Combined immunodeficiency, enteropathy spectrum
  • DOCK2 deficiency
  • Immunodeficiency by defective expression of human leukocyte antigen class 1
  • Lymphocyte count below reference range
  • Lymphocytopenia
  • Myelokathexis
  • Primary immunodeficiency with multifaceted aberrant lymphoid immunity
  • Primary immunodeficiency with natural killer cell deficiency and adrenal insufficiency
  • RIDDLE syndrome
  • Severe combined immunodeficiency due to CARD11 deficiency
  • Severe combined immunodeficiency due to CORO1A deficiency
  • Severe combined immunodeficiency due to DCLRE1C deficiency
  • Severe combined immunodeficiency due to deoxyribonucleic acid dependent protein kinase catalytic subunit deficiency
  • Severe combined immunodeficiency due to IKK2 deficiency
  • Severe combined immunodeficiency due to LAT deficiency
  • Severe T-cell immunodeficiency, congenital alopecia, nail dystrophy syndrome
  • Susceptibility to respiratory infection associated with CD8alpha chain mutation
  • T-cell negative B-cell positive severe combined immunodeficiency due to JAK3 deficiency
  • T-cell receptor alpha-beta-positive T-cell deficiency
  • Warts, hypogammaglobulinemia, infections, and myelokathexis

Diagnostic Related Group(s)

The code D81.89 is grouped in the following Diagnostic Related Group(s) MS-DRG V42.0

  1. Major Hematological And Immunological Diagnoses Except Sickle Cell Crisis And Coagulation Disorders With Mcc (808)
  2. Major Hematological And Immunological Diagnoses Except Sickle Cell Crisis And Coagulation Disorders With Cc (809)
  3. Major Hematological And Immunological Diagnoses Except Sickle Cell Crisis And Coagulation Disorders Without Cc/mcc (810)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
D81.89 Right Arrow 279.2 Combined immunity defic
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
D81 Combined immunodeficiencies
D81.0 Severe combined immunodeficiency [SCID] with reticular dysgenesis
D81.1 Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
D81.2 Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
D81.3 Adenosine deaminase [ADA] deficiency
D81.30 Adenosine deaminase deficiency, unspecified
D81.31 Severe combined immunodeficiency due to adenosine deaminase deficiency
D81.32 Adenosine deaminase 2 deficiency
D81.39 Other adenosine deaminase deficiency
D81.4 Nezelof's syndrome
D81.5 Purine nucleoside phosphorylase [PNP] deficiency
D81.6 Major histocompatibility complex class I deficiency
D81.7 Major histocompatibility complex class II deficiency
D81.8 Other combined immunodeficiencies
D81.81 Biotin-dependent carboxylase deficiency
D81.810 Biotinidase deficiency
D81.818 Other biotin-dependent carboxylase deficiency
D81.819 Biotin-dependent carboxylase deficiency, unspecified
D81.82 Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]
D81.9 Combined immunodeficiency, unspecified
This page was last updated on: 10/1/2024
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